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DeCS
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Descriptor English:
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Multiple System Atrophy
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Descriptor Spanish:
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Atrofia de Múltiples Sistemas
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Descriptor Portuguese:
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Atrofia de Múltiplos Sistemas
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Synonyms English:
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Atrophies, Multisystem
Atrophies, Multisystemic
Atrophy, Multiple System
Atrophy, Multisystem
Atrophy, Multisystemic
Multiple System Atrophies
Multiple System Atrophy Syndrome
Multisystem Atrophies
Multisystem Atrophy
Multisystemic Atrophies
Multisystemic Atrophy
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Tree Number:
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C10.177.575.550
C10.228.140.079.612
C10.228.662.550
C10.574.928.625
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Definition English:
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A syndrome complex composed of three conditions which represent clinical variants of the same disease process: STRIATONIGRAL DEGENERATION; SHY-DRAGER SYNDROME; and the sporadic form of OLIVOPONTOCEREBELLAR ATROPHIES. Clinical features include autonomic, cerebellar, and basal ganglia dysfunction. Pathologic examination reveals atrophy of the basal ganglia, cerebellum, pons, and medulla, with prominent loss of autonomic neurons in the brain stem and spinal cord. (From Adams et al., Principles of Neurology, 6th ed, p1076; Baillieres Clin Neurol 1997 Apr;6(1):187-204; Med Clin North Am 1999 Mar;83(2):381-92) |
Indexing Annotation English:
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a specific neurodegenerative syndrome complex; not for atrophy in other systems
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See Related English:
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Olivopontocerebellar Atrophies
Shy-Drager Syndrome
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History Note English:
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1998
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Allowable Qualifiers English:
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Record Number:
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33352
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Unique Identifier:
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D019578
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Occurrence in VHL:
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Similar:
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DeCS
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